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SGSH Rabbit pAb

Cat No.: APA3507
Size:
Product Name: SGSH Rabbit pAb
Cat No.: APA3507
source: Rabbit
reactivity: Human
applications: WB,IHC,ICC/IF
clonality: Polyclonal
recommended dilution: WB: 1:1000
IHC: 1:50
ICC/IF: 1:50
format: Liquid
isotype: IgG
immunogen: Recombinant protein of human SGSH
calculated molecular weight: 57 kDa
observed molecular weight: 57 kDa
genbank accession number: P51688
gene id (ncbi): 6448
purification method: Affinity Purification
conjugate: Un-conjugated
storage: Store at -20°C. Supplied in 50nM Tris-Glycine(pH 7.4), 0.15M NaCl, 40%Glycerol, 0.01% sodium azide and 0.05% BSA. Stable for 12 months from date of receipt.
synonyms: HSS; SFMD; MPS3A
category: Primary Ab
concentration: 0.5mg/ml
background: This gene encodes the enzyme sulfamidase; one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jun 2017]