Ornithine Carbamoyltransferase Rabbit pAb
Cat No.: APA1410
Size:
Product Name: | Ornithine Carbamoyltransferase Rabbit pAb |
Cat No.: | APA1410 |
source: | Rabbit |
reactivity: | Human, Mouse, Rat |
applications: | WB,IHC,IP |
clonality: | Polyclonal |
recommended dilution: | WB: 1:1000 IHC: 1:20 IP: 1:20 |
format: | Liquid |
isotype: | IgG |
immunogen: | A synthetic peptide of human Ornithine Carbamoyltransferase |
calculated molecular weight: | 40 kDa |
observed molecular weight: | 40 kDa |
genbank accession number: | P00480 |
gene id (ncbi): | 5009 |
purification method: | Affinity Purification |
conjugate: | Un-conjugated |
storage: | Store at -20°C. Supplied in 50nM Tris-Glycine(pH 7.4), 0.15M NaCl, 40%Glycerol, 0.01% sodium azide and 0.05% BSA. Stable for 12 months from date of receipt. |
synonyms: | OCTD |
category: | Primary Ab |
concentration: | 0.5mg/ml |
background: | This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also. [provided by RefSeq, Jul 2008] |